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Cystic fibrosis

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Search Period All yearsLast 12 monthsLast 5 years Topic All topicsGeneralNutrition and dietAlternative treatment methods Type of research Any type of researchHighest evidence only (96)Meta-analysis (21)Treatment guideline (8)Systematic review (33)Randomized trial (27)Phase 3 study (7)Clinical trial (707)Review article (354)Early study (phase 1 or 2) (16)Case report (129)Laboratory or animal study (55)Commentary or editorial (60) Studies currently recruiting participants only (30)

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Publications and studies (2553)

• Highly mucus permeating and zeta potential changing self-emulsifying drug delivery systems: A potent gene delivery model for causal treatment of cystic fibrosis. (2019/02/25) ♡
• A Neutralizing Aptamer to TGFBR2 and miR-145 Antagonism Rescue Cigarette Smoke- and TGF-β-Mediated CFTR Expression. (2019/02/06) ♡
• Integrative expression analysis identifies a novel interplay between CFTR and linc-SUMF1-2 that involves CF-associated gene dysregulation. (2019/02/05) ♡
• Precision toxicology shows that troxerutin alleviates ochratoxin A-induced renal lipotoxicity. (2019/02/01) ♡
• Meta-analysisiAll studies on one question combined and calculated together. This is the strongest form of research that exists: a single loose study can be coincidence, dozens together much less so. The label says something about the design, not about the outcome — which can also be that something does NOT work. Efficacy and Safety of CFTR Corrector and Potentiator Combination Therapy in Patients with Cystic Fibrosis for the F508del-CFTR Homozygous Mutation: A Systematic Review and Meta-analysis. (2019/02/01) ♡
• Patients with cystic fibrosis having a residual function mutation: Data from the Italian registry. (2019/02/01) ♡
• Ventilation inhomogeneity is associated with OGTT-derived insulin secretory defects in cystic fibrosis. (2019/02/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. The nutritional status in CF: Being certain about the uncertainties. (2019/02/01) ♡
• Recruitment manoeuvres dislodge mucus towards the distal airways in an experimental model of severe pneumonia. (2019/02/01) ♡
• [Protective effect of Yishen Tongluo Recipe against benzo(a)pyrene-induced sperm DNA methylation changes in male rats]. (2019/02/01) ♡
• A pathogenic role for cystic fibrosis transmembrane conductance regulator in celiac disease. (2019/01/15) ♡
• Persistence and Microevolution of Pseudomonas aeruginosa in the Cystic Fibrosis Lung: A Single-Patient Longitudinal Genomic Study. (2019/01/11) ♡
• Key Players and Individualists of Cyclic-di-GMP Signaling in Burkholderia cenocepacia. (2019/01/10) ♡
• Maintenance of S. aureus in Co-culture With P. aeruginosa While Growing as Biofilms. (2019/01/09) ♡
• Novel Pyoverdine Inhibitors Mitigate Pseudomonas aeruginosa Pathogenesis. (2019/01/09) ♡
• Genome-Based Approach Delivers Vaccine Candidates Against Pseudomonas aeruginosa. (2019/01/09) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Animal Models in the Pathophysiology of Cystic Fibrosis. (2019/01/04) ♡
• Characterization of Δ(G970-T1122)-CFTR, the most frequent CFTR mutant identified in Japanese cystic fibrosis patients. (2019/01/01) ♡
• Clinical trialiResearch in patients, without randomization between groups. Useful, but less certain than a randomized trial. Italian and North American dietary intake after ivacaftor treatment for Cystic Fibrosis Gating Mutations. (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Critical Care of the Adult Patient With Cystic Fibrosis. (2019/01/01) ♡
• EVALUATION OF NUTRITIONAL STATUS IN PATIENTS WITH CYSTIC FIBROSIS ACCORDING TO AGE GROUP. (2019/01/01) ♡
• Screening for Regulatory Variants in 460 kb Encompassing the CFTR Locus in Cystic Fibrosis Patients. (2019/01/01) ♡
• The effects of transfer from steady-state to tidally-changing salinities on plasma and branchial osmoregulatory variables in adult Mozambique tilapia. (2019/01/01) ♡
• Randomized researchiParticipants were divided into groups by lottery and compared with each other. This reduces the chance that a difference is due to something other than the treatment. A comprehensive evaluation of omega-3 fatty acid supplementation in cystic fibrosis patients using lipidomics. (2019/01/01) ♡
• Vitamin D intake, serum 25-hydroxy vitamin D and pulmonary function in paediatric patients with cystic fibrosis: a longitudinal approach. (2019/01/01) ♡
• Was the Last Ice Age dusty climate instrumental in spreading of the three "Celtic" diseases (hemochromatosis, cystic fibrosis and palmar fibromatosis)? (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Clinical metabolomics of exhaled breath condensate in chronic respiratory diseases. (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Protein stability and degradation in health and disease. (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Lung Transplant From Donor With Tracheal Bronchus: Case Report and Literature Review. (2019/01/01) ♡
• Surveillance Transbronchial Biopsy Program to Evaluate Acute Rejection After Lung Transplantation: A Single Institution Experience. (2019/01/01) ♡
• Description of individual patientsiThe story of one or a couple of patients. Informative, but you cannot infer from it whether something works in general. Lung Transplantation as Successful Treatment of End-stage Idiopathic Pleuroparenchymal Fibroelastosis: A Case Report. (2019/01/01) ♡
• Epstein-Barr Virus-Related Post-Transplant Lymphoproliferative Disorders in Cystic Fibrosis Lung Transplant Recipients: A Case Series. (2019/01/01) ♡
• Laboratory or animal researchiNo research in humans yet. Promising in a test tube or in mice unfortunately means nothing for patients. Establishment of a ΔF508-CF promyelocytic cell line for cystic fibrosis research and drug screening. (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Emerging Themes in PDZ Domain Signaling: Structure, Function, and Inhibition. (2019/01/01) ♡
• Description of individual patientsiThe story of one or a couple of patients. Informative, but you cannot infer from it whether something works in general. A rare clinical association: Barth syndrome and cystic fibrosis. (2019/01/01) ♡
• Clinical Development of Sphingosine as Anti-Bacterial Drug: Inhalation of Sphingosine in Mini Pigs has no Adverse Side Effects. (2019/01/01) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Advances in the diagnosis and management of pulmonary aspergillosis. (2019/01/01) ♡
• Two years of newborn screening for cystic fibrosis in Turkey: Çukurova experience. (2019/01/01) ♡
• Laboratory or animal researchiNo research in humans yet. Promising in a test tube or in mice unfortunately means nothing for patients. Functional characterization reveals that zebrafish CFTR prefers to occupy closed channel conformations. (2018/12/31) ♡
• Clinical trialiResearch in patients, without randomization between groups. Useful, but less certain than a randomized trial. A real life evaluation of non invasive ventilation in acute cardiogenic pulmonary edema: a multicenter, perspective, observational study for the ACPE SIMEU study group. (2018/12/29) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. [Molecular mechanisms of genistein action in the light of therapies for genetic and immunological diseases]. (2018/12/29) ♡
• Description of individual patientsiThe story of one or a couple of patients. Informative, but you cannot infer from it whether something works in general. Case 40-2018: A 47-Year-Old Woman with Recurrent Sinusitis, Cough, and Bronchiectasis. (2018/12/27) ♡
• Detection of viable but non-culturable Pseudomonas aeruginosa in cystic fibrosis by qPCR: a validation study. (2018/12/27) ♡
• Etiological involvement of CFTR in apparently unrelated human diseases. (2018/12/27) ♡
• Laboratory or animal researchiNo research in humans yet. Promising in a test tube or in mice unfortunately means nothing for patients. Effect of Trehalose Supplementation on Autophagy and Cystogenesis in a Mouse Model of Polycystic Kidney Disease. (2018/12/25) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Cystic Fibrosis of the Pancreas: The Role of CFTR Channel in the Regulation of Intracellular Ca(2+) Signaling and Mitochondrial Function in the Exocrine Pancreas. (2018/12/20) ♡
• Review articleiA summary of what is known about a topic, written by experts. Not compiled according to fixed search rules, so the selection of studies may be biased. Viral-Bacterial Co-infections in the Cystic Fibrosis Respiratory Tract. (2018/12/20) ♡
• Laboratory or animal researchiNo research in humans yet. Promising in a test tube or in mice unfortunately means nothing for patients. Variable Responses to CFTR Correctors in vitro: Estimating the Design Effect in Precision Medicine. (2018/12/19) ♡
• Respiratory Bacterial Culture Sampling in Expectorating and Non-expectorating Patients With Cystic Fibrosis. (2018/12/18) ♡
• Meta-analysisiAll studies on one question combined and calculated together. This is the strongest form of research that exists: a single loose study can be coincidence, dozens together much less so. The label says something about the design, not about the outcome — which can also be that something does NOT work. Recombinant growth hormone therapy for cystic fibrosis in children and young adults. (2018/12/17) ♡

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